关键词:Alpha-D-galactosidase A, Galactosylgalactosylglucosylceramidase GLA, GLA, Melibiase, Agalsidase, Alpha-D-galactoside galactohydrolase, Alpha-galactosidase A,Anti Fabrazyme/Agalsidase Alfa抗体|Fabrazyme/Agalsidase Alfa Antibody
α-D-半乳糖苷酶A、半乳糖酰半乳糖酰葡糖酰神经酰胺酶GLA、GLA、蜜二糖酶、阿加糖酶、α-D-半乳糖苷半乳糖水解酶、α-半乳糖苷酶 A
一 、产品描述
Fabrazyme/Agalsidase Alfa与天然α-半乳糖苷酶A相同的氨基酸序列。Fabrazyme/Agalsidase Alfa可用于法布里疾病的研究。
本品Fabrazyme/Agalsidase Alfa抗体具有高活性、高纯度、低内毒素、无多余标签等优势。
二 、产品详情
货号 |
DHC19529 |
适用物种 |
Human |
UniProt |
P06280 |
克隆性 |
Monoclonal |
CAS |
104138-64-9 |
应用 |
Research Grade Biosimilar |
靶点 |
Alpha-D-galactosidase A, Galactosylgalactosylglucosylceramidase GLA,GLA,Melibiase, Agalsidase, Alpha-D-galactoside galactohydrolase, Alpha-galactosidase A |
储存 |
Use a manual defrost freezer and avoid repeated freeze-thaw cycles. Store at 4°C short term (1-2 weeks). Store at -20°C 12 months. Store at -80°C long term. |
三、 已发表文献
Agalsidase Alfa. PMID: 30601613 |
Agalsidase beta (Fabrazyme) for Fabry disease. PMID: 12968124 |
Fabrazyme--recombinant protein treatment for Fabry's disease. PMID: 12080957 |
The Fabrazyme shortage--a call to action for metabolic physicians. PMID: 21111645 |
Agalsidase alfa: a review of its use in the management of Fabry disease. PMID: 22946754 |
Agalsidase alfa versus agalsidase beta for the treatment of Fabry disease: an international cohort study. PMID: 29437868 |
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